Synonyms of Desmoid Tumor
- Aggressive fibromatosis
- Deep fibromatosis
- Grade I fibrosarcoma
- Musculoaponeurotic fibromatosis
- Nonmetastasizing fibrosarcoma
Disorder SubdivisionsGeneral Discussion
The Greek word desmos which means tendon or band like has been the origin of the term desmoid and was coined by Muller in 1838. Desmoid tumor commonly develops in the fibrous (connective) tissue of the body that forms tendons and ligaments, usually in the arms, legs or midsection, and also in the head and neck. These tissues of the body connect, support, and surround other body parts and organs.
Desmoid tumor is also called as aggressive fibromatosis as it has similarities with a malignant (cancerous) tumor called fibrosarcoma however, it is considered benign because it does not metastasize (spread) to other parts of the body.
Regardless of its scientific classification, a Desmoid tumor can be invasive to surrounding tissues and difficult to control. Desmoid tumors can develop virtually at any body site. Superficial desmoids tend to be less aggressive than deep desmoids (abdominal, extra abdominal, mesenteric). It can adhere to and intertwine with surrounding structures and organs. The myofibroblast is the cell considered to be responsible for the development of Desmoid tumor and usually very difficult to remove because they intertwine extensively with the surrounding tissues. These tumors look like dense scar tissue and just like scar tissue, they adhere tenaciously to surrounding structures and organs.
Surgery has been the traditional main mode of therapy for Desmoid tumors but up to 70% of these tumors recur after surgery.Organizations related to Desmoid Tumor
- American Cancer Society, Inc.
1599 Clifton Road NE
Atlanta GA 30329
Phone #: 404-320-3333
800 #: 800-227-2345
Home page: http://www.cancer.org
- Desmoid Tumor Research Foundation
P.O. Box 273
Suffern NY 10901
Phone #: 914-262-6595
800 #: N/A
Home page: http://www.dtrf.org
- Madisons Foundation
PO Box 241956
Los Angeles CA 90024
Phone #: 310-264-0826
800 #: N/A
Home page: http://www.madisonsfoundation.org
For a Complete Report
This is an abstract of a report from the National Organization for Rare Disorders, Inc. ? (NORD). A copy of the complete report can be obtained for a small fee by visiting the NORD website. The complete report contains additional information including symptoms, causes, affected population, related disorders, standard and investigational treatments (if available), and references from medical literature. For a full-text version of this topic, see http://www.rarediseases.org/search/rdblist.html